Chondroectodermal dysplasia (Ellis-van Creveld syndrome): a case report

نویسندگان

  • Margarita Varela
  • Carmen Ramos
چکیده

A case of chondroectodermal dysplasia (Ellis-van Creveld syndrome) with a remarkable number of the classic oral and dental changes is described. This syndrome involves all embryonic tissue layers and is polysymptomatic; yet some oral and dental manifestations are pathognomonic and must be considered in primary diagnostic criteria. However, in some patients, these oral and dental manifestations are not clinically evident leading to misdiagnosis.

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Chondroectodermal dysplasia (Ellis-Van Creveld syndrome: A case report

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تاریخ انتشار 2009